Bladder exstrophy is a congenital defect of birth. Bladder exstrophy is a malformation of the bladder. Bladder exstrophy defect also includes a separation of the pelvic bones. It more often occurs in the boys. It is where a child is constant with the flexible tank on the outside of the lower abdomen. The disorder implies usually many systems in the body, including the urinary tract, the skeletal muscles and bones, and the digestive system. Bladder exstrophy is congenital and rare, occurring in only three on all the 100.000 births of phase. Males are affected 1.5 to 2.3 times more often than of the females.

In the female child, the urethra are shorter than usual, although the uterus, uterine trompex, and the ovaries are normal. In the male child, the testicles can appear undescended at the beginning, but with time the scrotum develops and the testicle almost always go down in a normal position. Bladder exstrophy requires surgical repair usually implying the reconstruction by stage. Several surgical options of treatment are available but they depend on the severity of the condition.

A form of treatment is a modern rebuilding by stages which implies the closing of the flexible tank and the basin during the time new-born child. Additional surgical procedures to improve the external genitals are almost always required. In selected cases where the flexible tank is good quality, the closing of the flexible tank and the rebuilding and the urethra can be combined in an operation. The boys and girls can require surgery on the pubis to recreate the normal distribution of hair. The goals of the therapy include the restoration of the urinary continence with the conservation of the renal function and the rebuilding of the functional genitals and a esthetic way acceptable.

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